Papillon- Lefèvre Syndrome: report of a case and its management
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Papillon- Lefèvre Syndrome: report of a case and its management

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Papillon- Lefèvre Syndrome: report of a case and its management

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dc.contributor.author Sachdeva, Shabina es
dc.contributor.author Kalra, Namita es
dc.contributor.author Kapoor, Pranav es
dc.date.accessioned 2014-05-21T12:15:12Z
dc.date.available 2014-05-21T12:15:12Z
dc.date.issued 2012 es
dc.identifier.uri http://hdl.handle.net/10550/35233
dc.source Sachdeva, Shabina ; Kalra, Namita ; Kapoor, Pranav. Papillon- Lefèvre Syndrome: report of a case and its management. En: Journal of Clinical and Experimental Dentistry, 2012, Vol. 4, No. 1: 77-81 es
dc.subject Odontología es
dc.subject Ciencias de la salud es
dc.title Papillon- Lefèvre Syndrome: report of a case and its management es
dc.type info:eu-repo/semantics/article en
dc.type info:eu-repo/semantics/publishedVersion en
dc.subject.unesco UNESCO::CIENCIAS MÉDICAS es
dc.description.abstractenglish Papillon-Lefèvre Syndrome (PLS) is a rare autosomal recessive disorder first described by two French physicians, Papillon and Lefèvre in 1924. The disorder is characterized by diffuse palmoplantar keratoderma and precocious aggressively progressing periodontitis, leading to the premature loss of deciduous and permanent teeth at a very young age. The cutaneous lesions are usually manifested simultaneously with the intra-oral presentations and include keratotic plaques on the palms and soles varying from mild psoriasiform scaly skin to overt hyperkeratosis. The etiopathogenesis of the syndrome is relatively obscure and immunologic, genetic or possible bacterial etiologies have been proposed. Due to the vast degree of periodontal breakdown involved at such an early age, the dental surgeon is often the first to diagnose the syndrome. This paper presents a clinical presentation a 15 year old male diagnosed with Papillon- Lefèvre Syndrome. es

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