Pycnodysostosis : a report of 3 clinical cases
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Pycnodysostosis : a report of 3 clinical cases

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Pycnodysostosis : a report of 3 clinical cases

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dc.contributor.author Alves Pereira, Daniela es
dc.contributor.author Berini Aytés, Leonardo es
dc.contributor.author Gay Escoda, Cosme es
dc.date.accessioned 2017-09-27T09:59:55Z
dc.date.available 2017-09-27T09:59:55Z
dc.date.issued 2008 es
dc.identifier.uri http://hdl.handle.net/10550/61177
dc.description.abstract Pycnodysostosis is a rare clinical entity, first described in 1962 by Maroteaux and Lamy. It is a genetic disorder, usually diagnosed at an early age. However, the diagnosis is sometimes late, made as a result of bone fracture, given the severe bone fragility resulting from increased bone density. Oral and maxillofacial manifestations of this disease are very clear. The head is usually large, the nose beaked, the mandibular angle obtuse, and both maxilla and mandible hypoplastic. Dental abnormalities and impaction are observed, as well as alterations in eruption and frequent dental crowding. The differential diagnosis is established with osteopetrosis, cleidocranial dysplasia and idiopathic acro-osteolysis. This article reviews the clinical and radiographic characteristics of pycnodysostosis based on three clinical cases of patients with this disease. es
dc.source Alves Pereira, Daniela ; Berini Aytés, Leonardo ; Gay Escoda, Cosme. Pycnodysostosis : a report of 3 clinical cases. En: Medicina oral, patología oral y cirugía bucal. Ed. inglesa, 13 10 2008: 4- es
dc.title Pycnodysostosis : a report of 3 clinical cases es
dc.type info:eu-repo/semantics/article en
dc.type info:eu-repo/semantics/publishedVersion en
dc.subject.unesco UNESCO::CIENCIAS MÉDICAS es
dc.identifier.doi es

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